ダウンロード数 : ?
ファイル
言語
英語
属性
症例報告
著者
堀江 宜佳
安部 翔子
内容記述(抄録等)
Carnitine palmitoyltransferase( CPT) II deficiency, a very rare inherited disorder of mitochondrial fatty acid oxidation, is characterized by myalgia attacks leading to rhabdomyolysis, hyperkalemia, and acute renal failure. Here, we report an anesthetic management in an infant patient with CPT II deficiency. A 16-month-old child underwent implantation of a totally implantable central venous access device. General anesthesia was performed with sevoflurane, fentanyl, and rocuronium. No complications occurred during the perioperative period. In patients with mitochondrial fatty acid oxidation disorders such as CPT II deficiency, it is important to ensure continuous glucose infusion with blood sugar monitoring. Avoiding drugs associated with rhabdomyolysis and maintaining normothermia are keys for safe anesthetic management.
主題
carnitine palmitoyltransferase (CPT) II deficiency
anesthetic management
pediatric anesthesia Correspondin
掲載誌名
Shimane Journal of Medical Science
37
2
開始ページ
61
終了ページ
65
ISSN
03865959
ISSN(Online)
24332410
発行日
2020-06
NCID
AA00841586
DOI
DOI(SelfDOI)
出版者
Faculty of Medicine, Shimane University
出版者別表記
島根大学医学部
資料タイプ
紀要論文
ファイル形式
PDF
権利関係
Faculty of Medicine, Shimane University
著者版/出版社版
出版社版
部局
医学部
他の一覧
このエントリーをはてなブックマークに追加