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language
eng
Attribute
Case Report
Author
HORIE, Yoshika
ABE, Shoko
Description
Carnitine palmitoyltransferase( CPT) II deficiency, a very rare inherited disorder of mitochondrial fatty acid oxidation, is characterized by myalgia attacks leading to rhabdomyolysis, hyperkalemia, and acute renal failure. Here, we report an anesthetic management in an infant patient with CPT II deficiency. A 16-month-old child underwent implantation of a totally implantable central venous access device. General anesthesia was performed with sevoflurane, fentanyl, and rocuronium. No complications occurred during the perioperative period. In patients with mitochondrial fatty acid oxidation disorders such as CPT II deficiency, it is important to ensure continuous glucose infusion with blood sugar monitoring. Avoiding drugs associated with rhabdomyolysis and maintaining normothermia are keys for safe anesthetic management.
Subject
carnitine palmitoyltransferase (CPT) II deficiency
anesthetic management
pediatric anesthesia Correspondin
Journal Title
Shimane Journal of Medical Science
Volume
37
Issue
2
Start Page
61
End Page
65
ISSN
03865959
ISSN(Online)
24332410
Published Date
2020-06
NCID
AA00841586
DOI
DOI(SelfDOI)
Publisher
Faculty of Medicine, Shimane University
Publisher Aalternative
島根大学医学部
NII Type
Departmental Bulletin Paper
Format
PDF
Rights
Faculty of Medicine, Shimane University
Text Version
出版社版
OAI-PMH Set
Faculty of Medicine
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