Shimane Journal of Medical Science

Shimane University Faculty of Medicine
ISSN :0386-5959(冊子体)
ISSN :2433-2410(オンライン)

クリエイティブ・コモンズ・ライセンス
これらの論文は クリエイティブ・コモンズ 表示 - 非営利 - 改変禁止 4.0 国際 ライセンスの下に提供されています。
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Shimane Journal of Medical Science 37 2
2020-06 発行

Anesthetic Management in an Infant Patient With Carnitine Palmitoyltransferase II Deficiency: A Case Report

堀江 宜佳
安部 翔子
ファイル
内容記述(抄録等)
Carnitine palmitoyltransferase( CPT) II deficiency, a very rare inherited disorder of mitochondrial fatty acid oxidation, is characterized by myalgia attacks leading to rhabdomyolysis, hyperkalemia, and acute renal failure. Here, we report an anesthetic management in an infant patient with CPT II deficiency. A 16-month-old child underwent implantation of a totally implantable central venous access device. General anesthesia was performed with sevoflurane, fentanyl, and rocuronium. No complications occurred during the perioperative period. In patients with mitochondrial fatty acid oxidation disorders such as CPT II deficiency, it is important to ensure continuous glucose infusion with blood sugar monitoring. Avoiding drugs associated with rhabdomyolysis and maintaining normothermia are keys for safe anesthetic management.
DOI
DOI(SelfDOI)
権利関係
Faculty of Medicine, Shimane University