File
language
eng
Attribute
Original article
Author
Shibata, Michiko Department of Otorhinolaryngology
Hamamura, Ryoji Department of Otorhinolaryngology
Aoi, Noriaki Department of Otorhinolaryngology
Kimura, Mitsuhiro Department of Otorhinolaryngology
Yamaguchi, Shuhei Department of Internal Medicine Ⅲ
Kawauchi, Hideyuki Department of Otorhinolaryngology
Description
Background: Spinocerebellar-degeneration (SCD) has been reported to show a variety of abnormal neurootological findings on electronystagmography (ENG) rather in a late stage of disease developing process, but not in an earlier stage.
Purpose: We have analysed ENG findings derived from 79 patients confirmed with SCD, in order to assess a diagnostic value of ENG and determine which manifestations are helpful in diagnosing SCD.
Results: We observed a high incidence of saccadic pursuit, severely impaired optokinetic nystagmus, and impaired visual suppression; observations that likely to be useful in diagnosing SCD. For each abnormal finding, we compared the data among patients with different types of SCD (olivopontocerebellar cortical atrophy, late cerebellar cortical atrophy, Shy-Drager syndrome, and hereditary SCD). We also studied the relationship between MRI findings and ocular abnormalities in these patients with SCD. In typical cases, the abnormal neuro-otological findings are effective in an earlier diagnosis of SCD.
Conclusion: In our present study, neuro-otological examinations are demonstrated to be useful for evaluating patients with SCD.
Subject
spinocerebellar-degeneration
neurootological examinations
magnetic resonance imaging
Journal Title
Shimane Journal of Medical Science
Volume
34
Issue
1
Start Page
21
End Page
26
ISSN
03865959
ISSN(Online)
24332410
Published Date
2017-07-31
NCID
AA00841586
Publisher
Faculty of Medicine, Shimane University
Publisher Aalternative
島根大学医学部
NII Type
Departmental Bulletin Paper
Format
PDF
Rights
Faculty of Medicine, Shimane University
Text Version
出版社版
OAI-PMH Set
Faculty of Medicine